Case Report
AcuteMyeloidLeukemiawithConcomitantBCR-ABLand
NPM1 Mutations
Benedetta Mariotti ,
1
FedericoMeconi ,
1
Raffaele Palmieri,
1
EleonoraDeBellis,
1
Serena Lavorgna,
1
TizianaOttone,
1
Vincenza Martini,
2
Francesco Lo-Coco,
1
andLauraCicconi
1
1
Department of Biomedicine and Prevention, University Tor Vergata, Rome, Italy
2
UOC Ematologia, Ospedale “Fabrizio Spaziani”, Frosinone, Italy
Correspondence should be addressed to Benedetta Mariotti; benedetta_mariotti@hotmail.it
Received 14 February 2019; Revised 26 March 2019; Accepted 31 March 2019; Published 11 April 2019
Academic Editor: Stephen Langabeer
Copyright © 2019 Benedetta Mariotti et al. is is an open access article distributed under the Creative Commons Attribution
License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is
properly cited.
We present a case report of a patient with acute myeloid leukemia (AML) characterized by the simultaneous presence of
nucleophosmin 1 (NPM1) mutation and the breakpoint cluster region-Abelson (BCR-ABL) fusion oncogene. Our findings
emphasize the importance of routinely including BCR-ABL in the diagnostic workup of AML in order to offer to the patients the
most appropriate risk category and treatment options.
1.Introduction
Mutations in the NPM1 gene are the most frequent genetic
abnormalities occurring in AML and are highly specific for
de novo AML [1]. e BCR-ABL fusion gene is the genetic
hallmark of chronic myeloid leukemia (CML) but can also be
found in approximately 30% of acute lymphoblastic leu-
kemia (ALL) and rarely in AML (0.3–2% of newly diagnosed
cases). In the updated WHO classification published in 2016,
AML with BCR-ABL has been introduced as a provisional
new entity [2, 3]. In BCR-ABL-positive AML, molecular and
cytogenetic profile may help to distinguish de novo AML
cases from CML-blastic phase (CML-BP).
To the best of our knowledge, the co-occurrence of BCR-
ABL fusion gene and NPM1 mutations in de novo AML has
been reported in only few cases [4]. Herein, we report a 74-
year-old patient diagnosed with AML harboring a complex
three-way translocation t(9;22;12)(q34;q13;q11) encoding
for two isoforms of BCR-ABL transcript (b3a2;b2a2) and a
concomitant type A mutation in the NPM1 gene.
2.CaseReport
A 74-year-old male, with a history of type II diabetes and
previous ischemic heart disease, was admitted on September
2014 to the emergency room of the hospital complaining
severe asthenia and nasal bleeding. ere was no previous
history of hematological disorders. Blood cell count dis-
closed Hb 6.4gr/dL (12.0–16.0g/dL), Plts 35 × 10
9
/L
(150–450 × 10
9
/L), a WBC of 62 × 10
9
(4.30–10.80 × 10
9
/L),
basophils <2% (0–1.5%), and with 50% of blasts. e co-
agulation profile showed INR 1.5 (0.8–1.2), fibrinogen
69mg/dL (200–400mg/dL), ATIII 77% (75–128%), and
D-dimer 10757ng/mL (0–500ng/mL), suggesting a dis-
seminated intravascular coagulopathy (DIC). Bone marrow
aspirate showed infiltration by 89% of hypergranular leu-
kemic blasts (Figures 1 and 2).
Immunophenotyping of the leukemic population
showed positivity for CD45, CD33, CD117, and MPO and
negativity for CD34, HLA-DR, CD13, and CD56, compatible
with a diagnosis of AML. Clinical examination showed mild
Hindawi
Case Reports in Hematology
Volume 2019, Article ID 6707506, 4 pages
https://doi.org/10.1155/2019/6707506