ACI (Acta Cardiologia Indonesiana) (Vol.6 No.2): 153-158 153 Acta Cardiologia Indonesiana Web page: jurnal.ugm.ac.id/v3/jaci Single Coronary Artery, A Coronary Anatomy Anomaly Arzia Pramadi Rahman*, NaharTaufiq, Hariadi Hariawan Department of Cardiology and Vascular Medicine, Faculty of Medicine, Public Health and Nursing Universitas Gadjah Mada, Yogyakarta, Indonesia ARTICLE INFO *Corresponding author email: arziarahman@gmail.com address: Jalan Farmako Sekip Utara, Yogyakarta, 55281 Indonesia Keywords: single coronary artery; anomaly; anatomy; intervention cardiology Manuscript submitted: May 4, 2020 Revised and accepted: August 6, 2020 ABSTRACT Coronary artery anomaly and variation is a group of congenital abnormality of the coronary artery with a wide variety of clinical manifestations. The cases are rare and usually found incidentally, but they become interesting because they are the second most causes for sudden cardiac death (SCD) in young adults participating in competitive sports. The number of cases of coronary artery anomaly is starting to rise as the number of cases undergoing invasive and non-invasive diagnosis procedure. Single coronary artery is a very rare congenital anomaly where there is only one coronary ostium to supply the whole heart. This anomaly usually occurs with other congenital anomaly. The symptoms may be unspecific from asymptomatic until SCD. This case report discusses about a patient with single coronary artery, its clinical approach, and the treatment options. INTISARI Anomali dan variasi arteri koroner merupakan kelompok kelainan kongenital arteri koroner dengan variasi dan manifestasi klinis yang cukup luas. Meskipun kasusnya relatif jarang dijumpai dan biasanya ditemukan secara tidak disengaja, kasus anomali dan variasi arteri koroner cukup menarik perhatian karena menjadi penyebab kematian mendadak terbanyak ke-2 pada dewasa muda yang berpartisipasi dalam olahraga kompetitif. Anomali arteri koroner mulai lebih sering dijumpai seiring meningkatnya jumlah pasien yang menjalani prosedur diagnosis invasive maupun pencitraan noninvasive. Arteri koroner tunggal merupakan anomali kongenital yang jarang dijumpai dimana hanya terdapat satu arteri koroner yang berasal dari satu ostium koroner untuk mengaliri seluruh jantung. Anomali ini biasanya disertai dengan adanya anomali kongenital yang lain. Gejala yang dijumpai pada pasien dengan arteri koroner tunggal sangat bervariasi, dari gejala yang ringan dan tidak spesifik sampai dengan sudden cardiac death (SCD). Pada laporan kasus ini kami membahas mengenai kasus anomali anatomi koroner berupa arteri koroner tunggal, pendekatan klinis serta pilihan penatalaksanaannya. Introduction Anomaly and variation of the coronary artery is a group of congenital abnormality of the coronary artery with a wide variety of clinical manifestations. The cases are rare and usually found incidentally, but they become interesting because they are the second most causes for sudden cardiac death (SCD) in young adults participating in competitive sports. 1 This coronary anomaly is usually found incidentally during diagnostic procedures or post- mortem examinations, with the prevalence of 0.019-0.4% of general population, and <3% of the whole coronary anomaly group. 2,3 The symptoms may be unspecific from asymptomatic until SCD. 4 The treatment options may be conservative medical treatment, percutaneous coronary intervention (PCI) with stenting, or surgical correction. 5 This case report discusses about a patient with single coronary artery, its clinical approach, and the treatment options. Case Presentation An 83 year-old woman was referred to the Cardiology Outpatient Clinic of Dr. Sardjito General Hospital with a pISSN:2460-5700 eISSN:2579-4345