Gaisbo« ck syndrome (polycythemia and hypertension)
revisited: results from the national inpatient
sample database
Parasuram Krishnamoorthy
a
, Akshaya Gopalakrishnan
a
, Varun Mittal
b
, Aditi Kalla
a
,
Leandro Slipczuk
a
, Janani Rangaswami
c
, Vincent M. Figueredo
a
, and Franz H. Messerli
d
Background: Polycythemia is characterized by increased
blood viscosity and a chronic inflammatory state possibly
giving rise to excessive thromboembolic events and
hypertensive cardiovascular disease. We aimed to study the
relationship between polycythemia and cardiac risk factors
using a large national registry.
Methods: Patients more than 18 years with a diagnosis of
polycythemia were identified from the National Inpatient
Sample 2009–2010 database using International
Classification of Diseases; Ninth Edition (ICD-9) code
238.4. Demographics, cardiac risk factors, and
cardiovascular events were identified.
Results: Polycythemia was present in 0.1% (n ¼ 37 922) of
hospital-discharged patients. Patients with polycythemia
had a significantly increased prevalence of all cardiac risk
factors and events, except for diabetes mellitus and
chronic kidney disease. Hypertension was more prevalent
in polycythemia compared to controls (61 vs. 46%;
P < 0.0001). After adjusting for age, sex, race, diabetes
mellitus, hyperlipidemia, tobacco use, obesity, coronary
artery disease, heart failure, and chronic kidney disease,
polycythemia was still a determinant of hypertension [1.37
(1.28–1.45); P < 0.001].
Conclusion: Polycythemia had high prevalence of all
cardiac risk factors and was independently associated with
increased prevalence of hypertension even after adjusting.
Our findings from the National Inpatient Sample provide
an epidemiological correlate of Gaisbo ¨ ck’s original
observation of the association of polycythemia and
hypertension more than a century ago.
Keywords: chronic inflammation, endothelial dysfunction,
hypertension, hyperviscosity, polycythemia
Abbreviations: CAD, coronary artery disease; CKD,
chronic kidney disease; CRP, C-reactive protein; ICD 9-CM,
International Classification of Diseases Ninth Edition Clinical
Modification; NIS, National Inpatient Sample
INTRODUCTION
P
olycythemia is characterized by increased blood
viscosity associated with microcirculatory disturban-
ces, including arterial and venous thromboses [1].
These thrombotic events often precede disease recognition.
Polycythemia is also described as a chronic inflammatory
state [2]. Chronic inflammation plays an important role in
vascular remodeling and atherosclerosis. Barbui et al. [2]
reported that blood levels of inflammatory biomarkers,
such as C-reactive protein (CRP), correlated with thrombo-
sis and the JAK2V617F allele burden in myeloproliferative
neoplasms such as essential thrombocythemia and polycy-
themia vera. Additionally, they also found that levels of
pentraxin-3, an anti-inflammatory marker, were inversely
associated with thrombotic events, suggesting vascular
inflammation plays an important role in polycythemia-
related thrombosis.
Several mechanisms have been postulated to explain this
pro-inflammatory state in polycythemia. Platelet and leu-
kocyte cellular activation, measured by overexpression of
CD11b antigen and by elevated plasma levels of serine
proteases cathepsin G, elastase, and myeloperoxidase [3],
result in increased production of cytokines and other pro-
inflammatory products. Endothelial dysfunction from vas-
cular inflammation has been observed in patients with
essential hypertension [4]. More than 25 years ago, Letcher
et al. [5] observed a direct relationship between blood
pressure and blood viscosity. The same group also showed
that whole blood viscosity was about 10% higher in unmed-
icated patients with relatively mild uncomplicated essential
hypertension than in apparently normal persons of compa-
rable age and gender taken from the same population [6].
Cinar et al., noted a 20% increase in blood pressure for a
physiologic compensation of 20% increased viscosity and
postulated that atherosclerotic vessels with decreased com-
pliance might benefit from treatment modalities aimed at
decreasing viscosity [7,8].
Journal of Hypertension 2018, 36:000–000
a
Division of Cardiology,
b
Division of Hematology-Oncology,
c
Department of Medicine,
Albert Einstein Medical Center, Philadelphia, Pennsylvania, USA and
d
Department of
Cardiology, Inselspital, University of Bern, Bern, Switzerland
Correspondence to: Parasuram Krishnamoorthy, MD, Chief Cardiology Fellow,
Einstein Medical Center, 5501 Old York Road, Levy 3232, Philadelphia, PA 19141,
USA. Tel: +1 732 501 5100; fax: +1 215 456 3533; e-mail: parasumk@yahoo.com
Received 2 November 2017 Revised 28 April 2018 Accepted 29 April 2018
J Hypertens 36:000–000 Copyright ß 2018 Wolters Kluwer Health, Inc. All rights
reserved.
DOI:10.1097/HJH.0000000000001805
Journal of Hypertension www.jhypertension.com 1
Original Article
Copyright © 2018 Wolters Kluwer Health, Inc. Unauthorized reproduction of this article is prohibited.