J Med Primatol. 2017;46:51–55. wileyonlinelibrary.com/journal/jmp
|
51 © 2017 John Wiley & Sons A/S.
Published by John Wiley & Sons Ltd
Accepted: 9 January 2017
DOI: 10.1111/jmp.12254
CASE REPORT
Spontaneous telangiectatc osteosarcoma in a rhesus macaque
(Macaca mulata)
B. Goldschmidt
1
| M.I.Z. Calado
1
| F.C. Resende
1
| R.M. Caldas
2
| L.W. Pinto
3
|
C.A.A. Lopes
1
| F.G.O. França
4
| B.S. Meireles
1
| I.V. Souza
1
1
Serviço de criação de primatas não
humanos, Insttuto de Ciência e Tecnologia em
Biomodelos (ICTB), Fundação Oswaldo Cruz
(FIOCRUZ), Rio de Janeiro, Brazil
2
Laboratório de Pesquisa Clínica
em Dermatozoonoses em Animais
Doméstcos, Insttuto Nacional de Infectologia
Evandro Chagas, Fundação Oswaldo Cruz, Rio
de Janeiro, RJ, Brazil
3
Divisão de Patologia, Insttuto Nacional de
Câncer, Rio de Janeiro, RJ, Brazil
4
Setor de radiologia, Nacional de Infectologia
Evandro Chagas, Fundação Oswaldo Cruz, Rio
de Janeiro, RJ, Brazil
Correspondence
Beatriz Goldschmidt, Serviço de criação de
primatas não humanos, Insttuto de Ciência e
Tecnologia em Biomodelos (ICTB), Fundação
Oswaldo Cruz (FIOCRUZ), Avenida Brasil, Rio
de Janeiro, Brazil.
Email: bibi@focruz.br
Abstract
Osteosarcoma (OS) is the most common type of bone cancer, especially in young.
Telangiectatc osteosarcoma (TO) is a rare variant of OS, and hence, its occurrence,
presentaton, and prognosis are poorly understood. A 4-year-old female rhesus mon-
key presentng lameness and swelling was examined for a mass on the right humerus.
Radiography revealed fracture and disorganized structure of bone tssue.
Histopathological examinaton revealed malignant neoplasm composed of anaplastc
osteoblasts, which invaded the bone marrow and surrounded blood-flled cysts in the
epiphysis and diaphysis forming septa. Cytogenetc analysis showed aneuploid cells,
supernumerary AgNORs, and a marker fragment. The neoplasm was diagnosed as TO.
To our knowledge, the occurrence of TO and its cytogenetc analysis were reported
for the frst tme in non-human primates.
KEYWORDS
bone cancer, chromosomes, non-human primate, osteosarcoma
1 | INTRODUCTION
Osteosarcoma (OS) is the most common primary malignant bone
tumor in humans, dogs, and cats.
1
In non-human primates, sponta-
neous OS is rarely described and only few cases can be found in the
literature in rhesus macaques (Macaca mulata).
2-4
Telangiectatc osteosarcoma (TO) is one of the rare subtypes of
OS. It accounts for about 3%-10% of all human OSs with a preponder-
ance of males and occurs mainly in the younger age group. The most
common locaton at presentaton is the metaphyses of long bones.
The distal femur is involved most frequently, followed in frequency
by the proximal tbia and proximal humerus.
5
This type of OS has not
been described in non-human primates. Although conventonal OSs
may contain telangiectatc elements, only those composed almost
entrely of telangiectatc tssue are generally considered true exam-
ples of this entty. The most common and most important diferental
diagnostc consideraton is aneurismal bone cyst (ABC). The radio-
graphic and gross appearances of TO and ABC show varying simi-
larites.
5
Another important diagnostc consideraton includes giant
cell tumor of bone. The histologic appearances of these enttes are
very diferent and are easily distnguishable from TO. The presence
of vascular spaces lined only by endothelial cells and the absence of
osteoid in the hemangiosarcoma are the key histologic features used
to diferentate hemangiosarcoma from TO that needs to be consid-
ered in the diferental diagnosis for a lytc bone tumor that appears
to be malignant. Telangiectatc osteosarcoma is an aggressive tumor
that destroys pre-existng bone and forms blood-flled cysts lined by
malignant osteoblasts that form septae, with or without producton
of osteoid.
1,5
Radiographically, TO appears as purely lytc destructve
lesions mainly located in the metaphyses and afectng the medullary
and cortcal bones, with poorly demarcated margins.
5
The exact cause
of TO is unknown; however in humans, the familial occurrence in
cousins suggests a genetc partcipaton.
6
The defniton of alteratons
has increased from visualizaton at the chromosome level to point
with OS mutatons, but the genetc etology of OS is stll unknown.
7
Conventonal cytogenetc studies have demonstrated that OS exhib-
its high karyotype heterogeneity, with diferent degrees of aneuploidy
and complex structural rearrangements. Although many cytogenetc