The Tessier No. 7 cleft is the least rare seen atypical craniofacial cleft. The incidence of the malformation is reported to be between 1: 3000 and 1: 5642 births (1). Males are more frequently affected than females. Bilateral involvement is rare. It has been termed as hemifacial microsomia (1), craniofacial microsomia (2), first and second branchial arch syndrome and otomandibular dysostosis (1). Clinical expression is variable. A preauricular skin tag can be present in microform cases. In it’s complete form, cleft begins as a macrostomia at the oral commissure and continuous across the cheek toward a microtic ear. All soft tissues may be underdeveloped on affected site. Osseous manifestations also cover a wide range. MATERIALS AND METHODS Five patients with Tessier No. 7 treated in our clinic, during the last 17 years, were evaluated. The age of admission was between 4 months to 12 years of age. All patients were female. There was no family history (Table 1). Table 1: Age and sex distribution of the patients. Sex Age Family History Female 4 months (-) Female 7 months (-) Female 11 months (-) Female 2 years (-) Female 12 years (-) There patients had the lateral fascial cleft on the left oral commisure and two had the deformity on the right (Figure 1a, Figure 2a, Figure 3a). Two patients had pretragal skin tag as associated deformity (2a, 3b). One of these two patients had bilateral prominant ear deformity and left, Puzansky type Ia hypoplastic mandibular ramus additionaly (Figure 3c). All patients were classified as type Ia, according to Harvold classification. Correction of the macrostomia was done according to Skoog technique (Table 2). JOURNAL OF ANKARA MEDICAL SCHOOL Vol 24, No 2, 2002 63-68 A RARE CRANİOFACİAL CLEFT: TESSIER NO. 7: A RETROSPECTIVE ANALYSIS Serdar Gökrem* ✥ Orhan Murat Özdemir* ✥ Arda Katırcıoğlu* ✥ Zeynep Şen* ✥ Atilla Ersoy* ✥ Zeki Can* ✥ Murat Emiroğlu* ✥ Serdar Gültan* ––––––––––––––––––––––––– * Ankara University, Medical School Department of Plastic and Reconstructive Surgery. –––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––––– Received: March 25, 2002 Accepted: Oct. 09, 2002 SUMMARY In this report we present a retrospective analysis of our craniofacial cleft cases, classified as Tessier no. 7. Key Words: Rare Craniofacial Clefts, Tessier No. 7 ÖZET Nadir Görülen Bir Kraniofasiyal Yarık: Tessier No. 7: Retros, Rektif Bir Analiz Bu yayında nadir görülen fasiyal yarıklardan, Tessier No. 7 olarak sınıflandırılan vakalarımızın retrospektif bir analizi bildirilmiştir. Anahtar Kelimeler: Nadir Görülen Fasiyal Yarıklar, Tessier No. 7