Matter et al. Diabetology & Metabolic Syndrome 2010, 2:23
http://www.dmsjournal.com/content/2/1/23
Open Access RESEARCH
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Research
Gradient-echo magnetic resonance imaging study
of pancreatic iron overload in young Egyptian
beta-thalassemia major patients and effect of
splenectomy
Randa M Matter*
1
, Khalid E Allam
2
and Amany M Sadony
1
Abstract
Background: Thalassemic patients suffer from diabetes mellitus secondary to hemosiderosis.
Aims: The study aimed to evaluate pancreatic iron overload by T2*-weighted Gradient-echo magnetic resonance
imaging (MRI) in young beta-thalassemia major patients and to correlate it with glucose disturbances, hepatic
hemosiderosis, serum ferritin and splenectomy.
Methods: Forty thalassemic patients (20 non diabetic, 10 diabetic, and 10 with impaired glucose tolerance) were
recruited from Pediatric Hematology Clinic, in addition to 20 healthy controls. All patients underwent clinical
assessment and laboratory investigations included complete blood count, liver function tests, serum ferritin and oral
glucose tolerance test (OGTT). A T2*-weighted gradient-echo sequence MRI was performed with 1.5 T scanner and
signal intensity ratio (SIR) of the liver and the pancreas to noise were calculated.
Results: Significant reduction in signal intensity ratio (SIR) of the liver and the pancreas was shown in thalassemic
patients compared to controls (P < 0.0001), Thalassemic patients with abnormal glucose tolerance; including diabetics
and thalassemics with impaired glucose tolerance; displayed a higher degree of pancreatic and hepatic siderosis
compared to thalassemics with normal glucose tolerance or controls (P < 0.001, P < 0.0001). Splenectomized
thalassemic patients had significantly lower SIR of pancreas compared to non splenectomized patients (P < 0.05). A
strong correlation was present between hepatic and pancreatic siderosis in studied patients (P < 0.001).
Conclusions: pancreatic siderosis can be detected by T2* gradient-echo MRI since childhood in thalassemic patients,
and is more evident in patients with abnormal glucose tolerance. After splenectomy, iron deposition may be
accelerated in the pancreas. Follow up of thalassemic patients using pancreatic MRI together with intensive chelation
therapy may help to prevent the development of overt diabetes.
Introduction
Thalassemic patients affected by systemic iron overload,
often die owing to iron induced failure of vital organs
such as heart and liver. Impairment of the endocrine and
exocrine function of the pancreas is a common complica-
tion in patients with beta-thalassemia major [1,2]. The
incidence of impaired glucose tolerance and diabetes in
thalassemia major patients varied from 9% to 15%
depending on the age of assessment, the intensity of
chelation, transfusion and related patient compliance
[3,4]. The etiology of diabetes in β-thalassemia is
increased peripheral resistance to insulin and direct toxic
effect of excess iron in the acinar and beta cells of pan-
creas resulting in insulin deficiency [5]. Structural abnor-
malities of the pancreas have been described on
sonography [1,6].
* Correspondence: randa_matar@yahoo.com
1
Department of Pediatrics, Faculty of Medicine, Ain Shams University, Cairo
11566, Egypt
Full list of author information is available at the end of the article