Turk Toraks Derg 2014; 15: 1-8
REVIEW
Expanding the Spectrum of Particle-and
Fiber-Associated Interstitial Lung Diseases
While interstitial lung disease (ILD) is common, less than fve percent of diagnoses appear to be related to occupational and environmental
exposures to particles and fbers; these injuries are most frequently recognized as pneumoconioses and hypersensitivity pneumonitides. As
a result of this small contribution to recognized ILD, the association of particles and fbers with this group of diseases is frequently deemed
of little consequence. However, it has been proposed that some portion of ILD without a recognized cause (i.e. idiopathic disease) can also
be related to exposures to particles and fbers. Many of these diagnoses are determined without beneft of microscopic examination of lung
tissue. Even when tissue is available, the conventional examination for the presence of particles and fbers is used. This approach employ-
ing optical microscopy is insensitive and leads to misdiagnosis. A review of previous investigation demonstrates associations of idiopathic
pulmonary fbrosis, desquamative interstitial pneumonia, pulmonary alveolar proteinosis, sarcoidosis, and eosinophilic granuloma with
particle and fber exposures. It is recommended that scanning electron microscopy in combination with the use of electron dispersive X-ray
analysis be employed whenever the question of a possible relationship between ILD and particle and fber exposure arises.
Key words: Pulmonary fbrosis, pulmonary alveolar proteinosis, sarcoidosis, eosinophilic granuloma
INTrodUCTIoN
Interstitial lung diseases (ILDs), a group also described as diffuse parenchymal lung diseases (DPLDs), includes over 200
distinct diseases in which the interstitium is altered by inflammation and/or fibrosis [1]. The interstitium of the lung is
comprised of the alveolar wall (and the lumen), vasculature, interstitial macrophages, fibroblasts, myofibroblasts, and
matrix components; the inflammatory and fibrotic disorders encompassed by ILD may affect any of these components.
The resulting infiltration by cellular and extracellular elements either causes distortion and destruction of the alveolar and
bronchiolar architecture or has little associated damage.
Interstitial lung disease is a diverse group of both acute and chronic disorders. Common clinical, radiographic, and
pathophysiologic features form the basis for collectively referring to this massive group of injuries as a single entity.
Frequently, the patient with ILD presents with the symptoms of dyspnea and nonproductive cough and crackles particu-
larly “Velcro rales” on physical examination. A chest radiograph shows reticular, nodular or mixed pattern markings and
lung function tests demonstrate some loss including decreased volumes and reduced diffusing capacity.
Interstitial lung disease is common and the diagnosis is established in about 70 out of every 100.000 individuals in the
United States [2]. About 10.000 Americans die every year from ILD [2]. This group of lung disorders includes disease
with both known and unknown causes. Less than five percent of ILD appears to be related to occupational and environ-
mental exposures to particles and fibers [3]. These injuries are most frequently recognized as pneumoconioses and
hypersensitivity pneumonitides and are almost always related to occupational exposures to particles and fibers. A diag-
nosis of work-related ILD is most frequently established on the basis of an occupational history, revealing a pertinent
exposure, and an abnormal chest x-ray.
As a result of the small contribution to recognized lung injury, the association of particles and fibers with ILD is fre-
quently deemed of little consequence. In the clinical setting or in the conduct of observational studies, a number of
factors may limit recognition of an association between a patient with idiopathic pulmonary fibrosis (IPF) and his or her
environmental and occupational exposures. These factors may include diagnostic misclassification, infrequent occur -
rence of IPF, exposure misclassification, and variation in susceptibility to exposures. However, it has been speculated that
some portion of that ILD without a recognized cause (i.e. idiopathic disease, which includes the majority of diagnoses
DOI: 10.5152/ttd.2014.3950
Andrew Ghio
1
, Rahul Sangani
1
, Victor Roggli
2
1
United States Environmental Protection Agency, NHEERL, Human Studies Facility, Chapel Hill/North Carolina, USA
2
Duke University, Duke University Medical Center, Department of Pathology, Durham/North Carolina, USA
Address for Correspondence: Andrew Ghio, United States Environmental Protection Agency, NHEERL, Human Studies
Facility, Chapel Hill/North Carolina, USA Phone: +1 919 9660670 E-mail: ghio.andy@epa.gov
©Copyright 2014 by Turkish Thoracic Society - Available online at www.toraks.dergisi.org
Abstract
Received: 05.09.2013 Accepted: 17.10.2013