113 A. Aghamohammadi, N. Rezaei (eds.), Clinical Cases in Primary Immunodeficiency Diseases, DOI 10.1007/978-3-642-31785-9_3, © Springer-Verlag Berlin Heidelberg 2012 A. Aghamohammadi, M.D., Ph.D. (*) Division of Clinical Immunology and Allergy, Research Center for Immunodeficiencies, Children’s Medical Center Hospital, Tehran University of Medical Sciences, Tehran, Iran H. Abolhassani, M.D., MPH • P. Mohammadinejad, M.D. • S. Pourhamdi, M.D. Department of Pediartrics, Research Center for Immunodeficiencies, Children’s Medical Center Hospital, Tehran University of Medical Sciences, Tehran, Iran N. Parvaneh, M.D. Department of Pediatrics, Research Center for Immunodeficiencies, Children’s Medical Center Hospital, Tehran University of Medical Sciences, Tehran, Iran Infectious Diseases Research Center, Tehran University of Medical Sciences, Tehran, Iran W. Al-Herz, M.D. Department of Pediatrics, Kuwait University, Kuwait, Kuwait A. Durandy, M.D., Ph.D. Unité d’Immunologie et Hématologie Pédiatrique, Institut National de la Santé et de la Recherche Médicale U768, Hôpital Necker Enfants Malades, Paris, France Faculté de Médecine, Université Paris Descartes, Paris, France M.M. Eibl, M.D. • H.M. Wolf, M.D. Department of Pediatrics, Immunological Outpatient Clinic, Biomedical Research Institute, Vienna, Austria T. Espanol, M.D., Ph.D. Department of Immunology and Immunodeficiencies, School of Medicine, University Hospital Vall d’Hebron, Barcelona, Spain H. Kanegane, M.D., Ph.D. • T. Miyawaki, M.D., Ph.D. Department of Pediatrics, Graduate School of Medicine and Pharmaceutical, University of Toyama, Toyama, Japan 3 Predominantly Antibody Deficiency Asghar Aghamohammadi, Hassan Abolhassani, Martha M. Eibl, Teresa Espanol, Hirokazu Kanegane, Toshio Miyawaki, Payam Mohammadinejad, Shabnam Pourhamdi, Hermann M. Wolf, Nima Parvaneh, Waleed Al-Herz, Anne Durandy, E. Richard Stiehm, and Alessandro Plebani