S141 Am J Clin Pathol 2018;149:S140-S149
DOI: 10.1093/AJCP/AQX127
© American Society for Clinical Pathology
AJCP / Meeting AbstrActs
neoplasms. As such, we compared patients with myeloid
disorders who underwent next-generation sequencing
(NGS) to compare the percentage of ring sideroblasts
and clinical features when SF3B1 variants were detected.
We identifed 13 patients with SF3B1 variants; 10 ran-
domly selected patients with myeloid neoplasms lacking
SF3B1 mutations were used as controls. SF3B1 variants
were identifed using a 25-gene panel and interrogated
via the Ion Torrent, while ring sideroblasts were quan-
titated using the aspirate. Age, sex, disease classifcation,
SF3B1 variant type, ring sideroblast percentage, and pro-
gression to acute leukemia were recorded for each sub-
ject. Among 13 patients with variant SF3B1, the mean
age was 73.5 years, 62% were women, and 92.3% were
still alive at the time of study. The majority (84.6%)
had variants in known SF3B1 “hotspots.” Of these 13
patients, nine (69.2%) met World Health Organization
criteria for a recognized myeloid neoplasm with ring sid-
eroblasts. Compared to controls, the mean percentage of
ring sideroblasts was signifcantly higher in patients with
any SF3B1 variant (31.2% vs 2.7%; P = .0011). Among
patients with SF3B1 variants in known hotspots, there
was a trend toward higher ring sideroblasts (mean 34.8%)
as compared to non-hotspot variants (mean 11.5%),
although numbers were too small for statistical com-
parisons. Subjects with any SF3B1variant and myeloid
neoplasm with ring sideroblasts had a lower incidence
of high-grade MDS and progression to acute leukemia
compared with controls. In summary, SF3B1 variants
correlated with an increased number of ring sideroblasts
independent of diagnosis. Given their unique attributes,
SF3B1-hostspot-positive myeloid neoplasms, particu-
larly those associated with MDS, may ultimately be best
characterized as a distinctive entity.
327
Evaluation of the Role of pAKT Expression in Epithelial
Mesenchymal Transition in Uterine Carcinosarcoma
Amir Momeni Boroujeni, MD, Elham Yousef, MD,
Ning Chen, MD, PhD, Raavi Gupta, MD; SUNY
Downstate Medical Center, Brooklyn, NY
Objectives: Epithelial-mesenchymal transition (EMT) has
been shown to be the underlying mechanism of the mor-
phologic variation of carcinosarcomas. EMT involves
loosening of epithelial adhesion structures and trans-
formation of epithelial cells into mesenchymal cells. It is
believed that EMT in uterine carcinosarcomas (UCSs) is
due to alterations of the AKT-pathway. Increased AKT
expression leads to modulation of expression of down-
stream genes, such as SLUG, leading to cytoskeletal and
cell-cell adhesion changes. Loss of E-cadherin expression
is the hallmark of EMT. In this study, we investigated the
role of AKT in EMT of UCS.
Methods: A total of 33 cases of UCS were selected, and
survival data were obtained. Immunohistochemical stain-
ing with E-cadherin (EP700Y, 1:200 dilution, Roche-
Ventana) and pAKT (ab8805, 1:350 dilution, Abcam)
was performed. Expression pattern of the antibodies was
assessed in the epithelial and mesenchymal components of
the tumor. Loss of E-cadherin in the mesenchymal com-
ponent was considered epithelial mesenchymal transition.
Staining of <20% cells was considered negative. Survival
data were compared using cox regression to determine the
prognostic signifcance of AKT expression.
Results: Of 33 cases, 28 showed loss of E-cadherin
expression in mesenchymal component. Fourteen of 28
cases (50%) showed increased expression of pAKT in
the mesenchymal component. Three of 28 cases (10.7%)
showed positivity of both components, and in 10/28 cases
(35.7%), both components were negative for pAKT. One
case showed positive pAKT staining in the epithelial com-
ponent and negative staining in the mesenchymal com-
ponent. Survival analysis showed no prognostic effect of
AKT expression.
Conclusion: AKT pathway is the main mechanism of epi-
thelial mesenchymal transition in UCS. Our results show
that AKT pathway alterations drive the EMT in 50%
of UCS cases. In other cases, alternative pathways such
as RHOA/ROCK pathway should be investigated. The
mechanism of EMT appears to have no effect on survival.
328
EBV and HHV1 Positive CNS Infammatory
Pseudotumor: A Case Report
Christian Salib, MD, Taliya Farooq, MD,
George Kleinman, MD; Westchester Medical Center/New
York Medical College, Valhalla
Infammatory pseudotumor (IPT) is a rare benign lesion
of unknown cause, commonly involving the lung and
orbit but found in virtually every body site. IPT was frst
described in 1954 based on imaging fndings that mim-
icked those of malignant tumors. This rare entity, which
consists of mixed infammatory cells and myofbroblas-
tic spindle cells, is often associated with Epstein-Barr
virus (EBV) positivity. Here we are presenting a case of a
56-year-old Hispanic woman with a history of headaches,
dizziness, and frequent falls. MRI of the head demon-
strated a right temporal lesion with enhancement along
the temporal convexity, extending into the insula. A lum-
bar puncture yielded atypical lymphocytes with increased
nuclear to cytoplasmic ratio, irregular nuclear contours,
and coarse chromatin. Cerebral spinal fuid fow cytome-
try revealed a mixed population of cells, including B-cells
expressing CD19, CD20, kappa, and lambda. A subse-
quent open biopsy revealed areas of dense, mixed infl-
trates consisting of lymphocytes, histiocytes, plasma cells
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