© 2016 Nature America, Inc., part of Springer Nature. All rights reserved.
NATURE MEDICINE VOLUME 22 | NUMBER 11 | NOVEMBER 2016 1
FOCUS ON PSYCHIATRIC DISORDERS PERSPECTIVE
Neuropsychiatric disorders such as autism spectrum
disorder (ASD), schizophrenia (SCZ) and bipolar disorder
(BPD) are of great societal and medical importance, but
the complexity of these diseases and the challenges of
modeling the development and function of the human brain
have made these disorders difficult to study experimentally.
The recent development of 3D brain organoids derived from
human pluripotent stem cells offers a promising approach for
investigating the phenotypic underpinnings of these highly
polygenic disorders and for understanding the contribution of
individual risk variants and complex genetic background to
human pathology. Here we discuss the advantages, limitations
and future applications of human brain organoids as in vitro
models of neuropsychiatric disease.
Neuropsychiatric disorders, such as ASD, SCZ and BPD, have a
devastating impact on patients’ lives and represent a heavy social
and economic burden for societies worldwide
1,2
. The complex
symptomatology of these diseases, which affect uniquely human
cognitive and behavioral traits, combined with their polygenic
etiology, the lack of objective biomarkers for diagnosis and the
limitations of current research models, have made these disorders
difficult to classify diagnostically and to study experimentally. Our
current understanding of the structural, cellular and circuit-level
abnormalities that affect the brains of patients with neuropsychiatric
disorders remains very superficial, and the development of modern
therapeutics has stalled
3
.
Recent years, however, have witnessed unprecedented genomic
studies of large cohorts of individuals with neuropsychiatric disor-
ders, which has led to the current wealth of data on the genetics of
these disorders
4,5
. With this has come the challenge of linking the rare,
highly penetrant mutations and complex genetic variation identified
in these studies to the neurobiological phenotypes reflective of disease
states, and the need for faithful and tractable experimental models has
taken center stage. It has become clear that whereas animal models
have proven valuable for studying single-gene mutations, the majority
of neuropsychiatric phenotypes involve heterogeneous combinations
of many alleles of small effect, which are extremely difficult to recreate
in animal models. In addition, conventional animal models, such as
rodents, are limited by inherent species differences in the development,
architecture and function of their brains. Primate models are
also needed, including models of the human brain, but the use of
endogenous human brain tissue is complicated by practical and ethical
concerns of tissue availability, expansion and manipulation.
Recent progress has enabled the development of cellular models
of the developing human brain via the generation of 3D brain
organoids derived from human pluripotent stem cells. Although
reductionist in nature, brain organoids have great potential to comple-
ment 2D cell culture models and animal studies to investigate aspects
of human brain development and pathology. In this Perspective, we
will focus on human pluripotent stem cell (hPSC)-derived in vitro
models of neuropsychiatric disease and provide a discussion of the
advantages, limitations and promise that 3D human brain organoids
could have as new cellular platforms for investigating psychiatric
disease origin and pathology, and, notably, for decoding the impact
of genetic variants associated with mental illness on human brain
development and function.
Neuropsychiatric disease and the need for experimental models
Neuropsychiatric disorders have been historically and are currently
classified on the basis of clinical symptoms; however, there is
considerable sharing of symptomatology and genetic risk across
current disorder definitions, and each diagnostic category (ASD,
BPD, SCZ, etc.) most likely represents a heterogeneous combina-
tion of underlying conditions. Indeed, these disorders might be
interrelated, as attested to by the high rate of comorbidity between
them and the frequency with which individuals of a single pedigree
and bearing the same risk alleles present with different clinically
defined syndromes
6
.
Neuropsychiatric disorders affect complex higher-order brain
functions that involve multiple cell types across different brain
regions, such as the prefrontal cortex, the thalamic reticular nucleus,
the thalamus and the basal ganglia, among others. Disease pheno-
types have been reported at scales ranging from gross architectural
changes and abnormal activity patterns that might reflect altered cir-
cuit function
7,8
to abnormal functioning of individual ion channels
9
.
As the cellular, molecular and genetic phenotypes of these disorders
are studied in ever-greater detail, it becomes increasingly apparent
that individual clinically defined disorders show great heterogeneity
across each of these modalities. The complexity of these disorders
has impeded progress on elucidating their etiology and pathogenesis;
consequently, our understanding of the structural, cellular
and circuit-level abnormalities that affect the brains of patients with
neuropsychiatric disorders remains superficial.
Department of Stem Cell and Regenerative Biology, Harvard University,
Cambridge, Massachusetts, USA. Correspondence should be addressed to
P.A. (paola_arlotta@harvard.edu).
Received 25 July; accepted 22 September; published online 26 October 2016;
doi:10.1038/nm.4214
The promises and challenges of human brain organoids as
models of neuropsychiatric disease
Giorgia Quadrato, Juliana Brown & Paola Arlotta