552 Electroencephalography and clinical Neurophysiology, 1989, 73:552-556
Elsevier Scientific Publishers Ireland, Ltd.
EEG 02404
Short communication
Sensorimotor and auditory central time in locked-in syndrome
E. Facco, P. Caputo, D. Fiore * and G.P. Giron
Lab. of Neurophysiology, Department of Anesthesiology and Intensive Care, University of Padua, Padua (Italy),
and * Department of Neuroradiology, Hospital of Padua, Padua (Italy)
(Accepted for publication: 20 July 1989)
Summary Motor evoked potentials (MEPs) following magnetic cortical stimulation, somatosensory evoked potentials from
median nerve (SEP) and auditory brain-stem responses (ABR) were recorded in a patient with locked-in syndrome during the acute
and chronic phases of the clinical course.
During the acute phase both ABR and SEP were normal. The MEP from the right upper limb showed a delayed and low voltage
potential, while that from the left upper limb was absent. The CT scan showed a ponto-mesencephalic hypodensity.
In the chronic phase the MEP from the left upper limb had reappeared and showed a normal latency, while the one from the right
upper limb worsened; at that time a new small left fronto-parietal hypodensity had appeared on CT scan, The combined use of MEP,
SEP and ABR was able to confirm that the brain-stem damage involved the pyramidal but spared the lemniscal pathways, while
MEP changes during the clinical course appeared to reflect both clinical and radiological findings.
Key words: Evoked potentials; Auditory evoked potential; Somatosensory evoked potential; Motor evoked potential; Locked-in
syndrome; Brain-stem
Short latency evoked potentials (SLEPs) can provide help-
ful information on pontine and midbrain function in patients
with brain-stem lesions (Noel and Desmedt 1975; Starr and
Hamilton 1976; Gilroy et al. 1977; Brown et al. 1981; Oh et al.
1981; Seales et al. 1981; Ragazzoni et al. 1982; Stern et al.
1982; Hammond et al. 1985; Kaji et al. 1985; Morocutti et al.
1985; Towle et al. 1985; Ferbert et al, 1988) and during
posterior fossa surgery for clipping of basilar aneurysms (Lam
et at. 1985). So far, SLEPs have been recorded only in a few
cases of locked-in syndrome, showing abnormalities of both
auditory brain-stem responses (ABRs) and somatosensory
evoked potentials (SEPs) in most patients (Noel and Desmedt
1975; Starr and Hamilton 1976; Gilroy et al. 1977; Brown et
al. 1981; Oh et ak 1981; Seales et al. 1981; Stern et al. 1982;
Kaji et al. 1985; Towle et ak 1985; Ferbert et al. 1988), while
no data are available in the literature on motor evoked poten-
tials (MEPs).
In this paper we report a case of locked-in syndrome whose
MEP, ABR and SEP from median nerve were recorded during
the acute and chronic phases of the clinical course.
Correspondence to: E. Facco, M.D., Ist. Anestesiologia e
Rianimazione, Universit~t di Padova, Via C. Battisti 267, 35121
Padua (Italy).
Patient and methods
The patient was a 56-year-old man who suddenly presented
dysarthria and weakness of the left limbs followed by aniso-
coria. In a few hours he showed bilateral myosis, loss of
horizontal eye movements, hypertonus, quadriplegia and res-
piratory failure as well, but remained able to open his eyes on
command. He was intubated and submitted to mechanical
ventilation. The CT scan disclosed a ponto-mesencephalic hy-
podensity (Fig. 1A, B).
During the clinical course the patient underwent severe
extracranial complications (bronchopneumoma. pneumo-
thorax, sepsis and reversible cardiac arrest) from which he
recovered.
After 2 months from the attack the neurological condition
began to improve slightly: the patient showed weak movements
of the upper limbs and left leg, partial recovery of ocular and
facial movements. Afterwards the respiratory function progres-
sively improved, allowing the removal of mechanical ventila-
tion. The CT scan performed in the chronic phase, after the
patient recovered from the extracranial complications, showed
a new small hypodensity in the left fronto-parietal region (Fig.
1C. D). The patient was discharged from the intensive care
unit 6 months after the attack.
lhe SLEPs were recorded on the 10tb hospital day (before
the occurrence of cardiac arrest) and after 5 months.
0013-4649/89/$3.50 © 1989 Elsevier Scientific Publishers Ireland, Ltd.