Baclofen Treatment for Pain in Non-functional Children with Cerebral Palsy –A
Brief Report
Hilla Ben-Pazi
1
*, Gila Ben-Shimol
2
, Ruth David
2
, Adi Aran
3
and Natali Dechtiar
2
1
Pediatric Movement Disorders, Neuropediatric Unit, Shaare Zedek Medical Center, Jerusalem, Israel
2
Aleh nursery home, Jerusalem, Israel
3
Neuropediatric Unit, Shaare Zedek Medical Center, Jerusalem, Israel
*
Corrsponding Autor: Ben-Pazi H, Pediatric Movement Disorders, Neuropediatric Unit, Shaare Zedek Medical Center POB 3235, Jerusalem 91031, Israel, Tel:
9722-6555345; Fax: 9722-6555672; E-mail: benpazi@gmail.com
Rec date: January 7, 2016; Acc date: March 5, 2016; Pub date: March 14, 2016
Copyright: © 2016 Ben-Pazi H, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted
use, distribution, and reproduction in any medium, provided the original author and source are credited.
Abstract
Baclofen, a GABA-B agonist, reduces hypertonia by increasing spinal inhibition and improves motor function in
functional children with cerebral palsy. We hypothesized that oral baclofen reduces pain and improves daily care in
nonfunctional children with spastic cerebral palsy. To test this children residing in nursery homes with hypertonia
causing pain or interfering with daily care were enrolled in this randomized, double blind, placebo controlled,
crossover pilot study. Participants were examined before, during and after 13 weeks of baclofen (2 mg/kg/day) and
placebo for pain (Brief Pain Inventory and Dalhousie Pain Survey), ease of care (care and comfort questionnaire)
and overall treatment assessment (specific questionnaire, designed for this study). Two participants completed this
pilot (ages 7 and 8 years). Pain was reported to interfere less on peak dose of baclofen treatment compared to
placebo in one child (p=0.0001) and care tended to be easier in the other (p=0.05). Blinded caregivers
recommended continuing baclofen. No significant side effects were reported. Baclofen, an inexpensive safe
medication, may alleviate pain in nonfunctional spastic children.
Keywords: Brief Pain Inventory and Dalhousie Pain Survey; Care
and comfort questionnaire; Hypertonia; Range of motion; Nursery
home
Introduction
Recurrent and chronic pain of moderate intensity has been
documented in most children sufering from cerebral palsy (CP,) the
common cause of disability in children (2:1000 live births). Te spastic,
hypertonic element of this congenital motor disorder may be one an
important source of pain. 70% of children with CP experience
recurrent chronic pain of moderate intensity on a daily or weekly basis
[1,2]. Physiotherapy required on a daily basis involves painful exercises
and may be limited by pain. Pain evaluation in children is generally
based on childrens' report or parents' impression. However, in severely
disabled children with limited communication, pain assessment is
challenging. Difculty in pain evaluation may lead to underestimation
of pain resulting in under or over treatment. However, in these
children with hypertonia and limited communication one may
estimate pain indirectly by ease of daily care and child's comfort.
Baclofen, a GABA-B receptor agonist, is one of few medications
reducing hypertonia in CP [3]. Oral baclofen was found efective in
improving daily function in children with CP in a randomized double
blind study [4] and Intrathecal baclofen has been shown to alleviate
pain in 50% of patients thus improving daily care and communication
in severely afected children [5]. Nevertheless need for baclofen
treatment, its efcacy and impact on daily life in nonfunctional
children with CP has not been studied. Oral baclofen treatment is safer
and cheaper than intrathecal administration; however, its impact on
hypertonia related pain has not been formally evaluated in
nonfunctional children with CP. Te goal of this study was to assess
efectiveness of oral baclofen in reducing pain and improving daily care
in nonfunctional hypertonic children with CP. To test this we started a
prospective double blind randomized crossover pilot.
Case report
Participants: Children from nursery homes who were nonfunctional
(Gross-Motor-Function-Classifcation-System level 5) and sufered
from hypertonia that caused pain or difculty in daily care were
enrolled (n=3) and completed (n=2) the study:
Child #1, a 7-year-old girl was born afer 34 weeks of gestation with
low apgar scores (6 at 5 minutes). Her MRI demonstrated difuse
extensive encephelomalacia. Parents were second degree cousins;
infectious, genetic and metabolic workup was negative. She was blind
with no voluntary movements but occasionally reacted to her name.
Seizures were treated with lamotrigene. On examination she smiled
occasionally and initiated random vocalization. She had some dystonia
in her upper limbs. Spasticity was most prominent in lower limbs with
a positive Babinsky sign and clonus. Treatment with levodopa was
inefective.
Child #2, an 8-year-old boy, was born afer 32 weeks of gestation, to
non-consanguineous parents. He had non-progressive spastic
quadriplegia due to an unknown cause. He did not have any voluntary
movements or any apparent communication. During examination he
tended to fxate his gaze to the right with intermittent nystagmus.
Dystonic hand posture increased when excited. He had generalized
spasticity hyperactive deep tendon refexes and Babinski sign was
negative.
Child #3, a 7.5-year-old boy, was resuscitated following a domestic
accident at infancy. Seizures were treated with Phenobarbital. His only
Ben-Pazi H, et al, J Pediatr Neurol Med 216, 1:2
DOI: 10.4172/2472-100x.1000108
Case Report Open Access
J Pediatr Neurol Med, an open access journal
ISSN:2472-100x
Volume 1 • Issue 2 • 108
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ISSN: 2472-100X
Journal of Pediatric Neurology &
Medicine