76 AJR:194, January 2010
patients (92%) with pyothorax-associated
lymphoma had a history of artificial pneu-
mothorax therapy. Narimatsu et al. [4] re-
ported that 78 of 98 patients (80%) had a
similar history.
According to the literature, the mean age at
diagnosis of pyothorax-associated lymphoma
is approximately 60 years, and there is a predi-
lection for men [1–4]. Common symptoms in-
clude chest pain, fever, and a palpable chest
wall mass, which occur in approximately one
half of patients. Respiratory symptoms such as
productive cough, hemoptysis, and dyspnea
are found in one fourth of patients [1, 2, 4].
Aozasa [5] reported a 2% incidence of pyotho-
rax-associated lymphoma among patients with
concomitant chronic empyema. The current
pathophysiologic understanding of the dis-
ease suggests that both chronic Epstein-Barr
virus (EBV) infection and an immunocom-
Pyothorax-Associated Lymphoma:
Imaging Findings
Takuya Ueda
1
Christe Andreas
1
Jun Itami
2
Kunihisa Miyakawa
3
Hajime Fujimoto
4
Hisao Ito
5
Justus E. Roos
1
Ueda T, Andreas C, Itami J, et al.
1
Department of Radiology, Stanford University School
of Medicine, 300 Pasteur Dr., Rm. S-072, Stanford, CA
94305. Address correspondence to T. Ueda
(takueda-rad@umin.ac.jp).
2
National Cancer Center Hospital, Tokyo, Japan.
3
Nagano PET and Diagnostic Center, Nagano, Japan.
4
Department of Radiology, Numazu City Hospital,
Shizuoka, Japan.
5
Department of Radiology, Graduate School of Medicine,
Chiba University, Japan.
CardiopulmonaryImaging•OriginalResearch
AJR 2010; 194:76–84
0361–803X/10/1941–76
© American Roentgen Ray Society
P
yothorax-associated lymphoma
is a rare type of lymphoma that
typically occurs in patients who
have undergone artificial pneu-
mothorax therapy for tuberculosis [1–4]. Re-
sults of several studies [1–4] have suggested
that the development of pyothorax-associat-
ed lymphoma is triggered by long-standing
empyema, that is, lasting for more than 20
years after the initial pneumothorax treat-
ment. Until approximately 1970, artificial
pneumothorax therapy for tuberculosis was
performed mainly on younger patients. This
treatment was gradually replaced by clini-
cally more effective chemotherapy. A long
latency period between the artificial pneu-
mothorax treatment and the development of
pyothorax-associated lymphoma, sometimes
more than 40 years, has been reported [1–4].
Nakatsuka et al. [2] reported that 98 of 106
Keywords: CT, empyema, pleura, pyothorax-associated
lymphoma, tumors
DOI:10.2214/AJR.09.2603
Received February 19, 2009; accepted after revision
July 12, 2009.
OBJECTIVE. The purpose of this study was to evaluate the radiologic features of pyotho-
rax-associated lymphoma on CT scans and chest radiographs.
MATERIALSANDMETHODS. Radiographs and CT scans of 21 patients with bi-
opsy-proven pyothorax-associated lymphoma (17 men, four women; median age, 71 years;
range 52–77 years) were retrospectively identified. Two readers in consensus analyzed the
morphologic imaging features of pyothorax-associated lymphoma and determined their re-
lation to the preexisting chronic empyema cavity. In 13 cases, gallium scans were available
and were reviewed.
RESULTS. Sixteen patients had a history of artificial pneumothorax therapy for tubercu-
losis. Pyothorax-associated lymphoma was visualized mainly (71.4% of cases) as extrapul-
monary pleural masses on chest radiographs. The CT features included a lenticular (60%) or
crescentic (20%) soft-tissue mass located eccentrically at the margin of a coexistent empy-
ema cavity, which was present in all cases. Masses of pyothorax-associated lymphoma were
commonly located in the lateral costal pleura (50%) or at the costophrenic angle (30%). The
tumor matrix often appeared heterogeneous and contained areas of necrosis (60%). Direct in-
vasion of the chest wall, ribs, lung parenchyma, and abdomen was found in 75%, 50%, 25%,
and 25% of patients. Gallium scans, when available, showed marked uptake in 10 of 13 pa-
tients (76.9%).
CONCLUSION. In patients who have undergone artificial pneumothorax therapy for tu-
berculosis more than 20 years in the past, a pleural soft-tissue mass adjacent to the margin of a
coexistent empyema cavity suggests the presence of pyothorax-associated lymphoma. Knowl-
edge of the typical radiologic findings and locations of pyothorax-associated lymphoma help
in the diagnosis of this rare pathologic entity.
Ueda et al.
Pyothorax-Associated Lymphoma
Cardiopulmonary Imaging
Original Research
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